A condition marked by progressive CEREBELLAR ATAXIA combined with MYOCLONUS usually presenting in the third decade of life or later. Additional clinical features may include generalized and focal SEIZURES, spasticity, and DYSKINESIAS. Autosomal recessive and autosomal dominant patterns of inheritance have been reported. Pathologically, the dentate nucleus and brachium conjunctivum of the CEREBELLUM are atrophic, with variable involvement of the spinal cord, cerebellar cortex, and basal ganglia. (From Joynt, Clinical Neurology, 1991, Ch37, pp60-1)

Descriptor ID	D002527
MeSH Number(s)	C10.228.140.252.700.250 C10.228.854.787.500 C10.574.500.825.250 C16.320.400.780.500
Concept/Terms	Myoclonic Cerebellar Dyssynergia Myoclonic Cerebellar Dyssynergia Cerebellar Dyssynergia, Myoclonic Cerebellar Dyssynergias, Myoclonic Dyssynergia, Myoclonic Cerebellar Dyssynergias, Myoclonic Cerebellar Myoclonic Cerebellar Dyssynergias Dentate Cerebellar Ataxia Ataxia, Dentate Cerebellar Ataxias, Dentate Cerebellar Cerebellar Ataxias, Dentate Dentate Cerebellar Ataxias Dentate Cerebellar Atrophy Atrophies, Dentate Cerebellar Atrophy, Dentate Cerebellar Cerebellar Atrophy, Dentate Dentate Cerebellar Atrophies Dentate Nucleus Syndrome, Ramsay Hunt Ramsay Hunt Dentate Syndrome Dyssynergia Cerebellaris Progressiva Ramsay Hunt Cerebellar Syndrome Cerebellar Dyssynergia Cerebellar Dyssynergias Dyssynergia, Cerebellar Dyssynergias, Cerebellar Dyssynergia Cerebellaris Myoclonica Cerebelloparenchymal Disorder V Cerebelloparenchymal Disorder V Spinodentate Atrophy Dyssynergia Cerebellaris Myoclonica Of Hunt

Below are MeSH descriptors whose meaning is more general than "Myoclonic Cerebellar Dyssynergia".

Below are MeSH descriptors whose meaning is related to "Myoclonic Cerebellar Dyssynergia".

Below are MeSH descriptors whose meaning is more specific than "Myoclonic Cerebellar Dyssynergia".